Regional odontodysplasia (RO) is an unusual, non-hereditary anomaly of the dental hard tissues with typical clinical and radiographic features. RO is a rare developmental anomaly involving both mesodermal and ectodermal dental components of teeth. The primary and permanent dentitions of maxilla, mandible or both the jaws are involved. Most of the cases seen in females involving single quadrant of maxillary arch. Here we report a unique case of RO involving maxillary arch crossing midline in a 9-year old boy.
Key words: Odontodysplasia, Ghost teeth, Development anomaly.